Brief Report: Repetitive Behaviour Profiles in Williams syndrome: Cross Syndrome Comparisons with Prader–Willi and Down syndromes

Royston, Rachel, Oliver, Chris, Moss, Jo, Adams, Dawn, Berg, Katie, Howlin, Patricia, Nelson, Lisa, Burbidge, Cheryl, Stinton, Chris and Waite, Jane (2018). Brief Report: Repetitive Behaviour Profiles in Williams syndrome: Cross Syndrome Comparisons with Prader–Willi and Down syndromes. Journal of Autism and Developmental Disorders, 48 (1), 326–331.

Abstract

This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader–Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader–Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.

Publication DOI: https://doi.org/10.1007/s10803-017-3319-6
Divisions: Life & Health Sciences > Psychology
Life & Health Sciences > Applied Health Research Group
Life & Health Sciences
Published Date: 2018-01
Authors: Royston, Rachel
Oliver, Chris
Moss, Jo
Adams, Dawn
Berg, Katie
Howlin, Patricia
Nelson, Lisa
Burbidge, Cheryl
Stinton, Chris
Waite, Jane ( 0000-0002-8676-3070)

Download

[img]

Version: Published Version

Access Restriction: Restricted to Repository staff only


Export / Share Citation


Statistics

Additional statistics for this record